|Women with PKU need to follow a strict diet while pregnant to avoid serious birth defects.|
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Low-Phenylalanine Eating Pattern
- Drinking phenylalanine-free medical formula, which provides calories, protein, vitamins, and minerals without phenylalanine. Phenylalanine-free medical formulas are manufactured for infants, children, and adults and are the most important feature of the diet for PKU.
- Starches, including bread, potatoes, corn, and beans must be limited.
- Eliminating high-protein foods such as milk, meat, fish, chicken, pork, eggs, beans, and nuts.
- Eliminating foods and beverages made with aspartame, an artificial sweetener that contains phenylalanine.
National PKU News http://www.pkunews.org
NIH Genetics Home Reference http://ghr.nlm.nih.gov
Canadian PKU and Allied Disorders http://canpku.org
Caring for Kids—Canadian Paedatric Society http://www.caringforkids.cps.ca
What is PKU? University of Washington PKU Clinic website. Available at http://depts.washington.edu/pku/about/whatispku.html. Accessed August 10, 2015.
Phenylketonuria (PKU) EBSCO DynaMed website. Available at: http://www.ebscohost.com/dynamed. Updated July 24, 2014. Accessed August 10, 2015.
Phenylketonuria: screening and management [National Institutes of Health Consensus Statement, October 16-18, 2000]. National Institutes of Health website. Available at https://consensus.nih.gov/2000/2000Phenylketonuria113html.htm. Accessed August 10, 2015.
1/21/2014 DynaMed's Systematic Literature Surveillance http://www.ebscohost.com/dynamed: Lindegren ML, Krishnaswami S, Fonnesbeck C, et al. Adjuvant treatment for phenylketonuria (PKU). Comparative Effectiveness Reviews. 2012;56.
- Reviewer: Michael Woods, MD
- Review Date: 08/2015 -
- Update Date: 01/21/2014 -